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Surgery on Children

Surgery on Children Journal aims to publish issues related to Pediatric Surgery, Pediatric Neurosurgery, Pediatric Plastic Surgery, Pediatric Cardiovascular Surgery, Pediatric Orthopedic Surgery, Pediatric Vascular Surgery, Pediatric Gynecology and Obstetrics, Pediatric Ear Nose Throat, Ophthalmology, Pediatric Anesthesiology and Reanimation, Pediatric Urology, Pediatric Surgical Intensive Care Clinic, and other clinical surgery fields on children of the highest scientific and clinical value at an international level and accepts articles on these topics.

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Case Report
Nutritional and dietary approach in the post-surgical follow-up of hirschsprung disease: a case report
Abstract
Hirschsprung disease (HD) is a congenital condition caused by abnormal development of the enteric nervous system during the embryonic period, characterized by colonic aganglionosis. Total Colonic Aganglionosis (TCA) refers to the involvement of the entire colon extending to the terminal ileum, accounting for 3–12% of all HD cases. A 45-month-old male patient presented to the clinic with complaints of frequent vomiting and more than 10 watery diarrhea episodes per day. The patient's medical history revealed the development of short bowel syndrome (SBS) following Total Colonic Aganglionosis. Physical examination indicated a poor general condition, decreased skin turgor and tonus, along with growth and developmental delay. Laboratory findings demonstrated low sodium (Na) and potassium (K) levels with electrolyte imbalances. A low-carbohydrate, high-protein diet was planned alongside hydration therapy. Additionally, the family was educated on nutritional management and avoiding harmful foods. Following 17 days of treatment and dietary interventions, the patient's weight increased by 1.5 kg, and complaints of diarrhea and vomiting subsided. During a two-year follow-up period, a reduction in hospitalization frequency and improvements in the patient’s overall clinical condition were observed. The individualized treatment and nutritional plan significantly enhanced the patient’s quality of life. The management of short bowel syndrome, which may develop after HD surgery, requires individualized nutritional plans, a multidisciplinary approach, and continuity in patient-family education, all of which are critically important.

Keywords : Hirschsprung disease, pediatric surgery, nutrition and diet, short bowel syndrome

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Article available in :
Volume 2, Issue 3, 2025
Page : 114-117
https://doi.org/10.51271/SOC-0047
Article Information
Received : 13 Kas 2024
Accepted : 27 Ara 2024
Published : 01 Tem 2025
Corresponding Author :

Kübra Taşdan: Department of Nutrition, Faculty of Medicine, Yozgat Bozok University, Yozgat, Turkiye

[email protected]
Citation : Taşdan K. Nutritional and dietary approach in the post-surgical follow-up of Hirschsprung disease: a case report. Surg Child. 2025;2(3):114-117.

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