SOC

Surgery on Children Journal aims to publish issues related to Pediatric Surgery, Pediatric Neurosurgery, Pediatric Plastic Surgery, Pediatric Cardiovascular Surgery, Pediatric Orthopedic Surgery, Pediatric Vascular Surgery, Pediatric Gynecology and Obstetrics, Pediatric Ear Nose Throat, Ophthalmology, Pediatric Anesthesiology and Reanimation, Pediatric Urology, Pediatric Surgical Intensive Care Clinic, and other clinical surgery fields on children of the highest scientific and clinical value at an international level and accepts articles on these topics.

EndNote Style
Index
Case Report
A rare case of primary pulmonary embryonal rhabdomyosarcoma in children
Rhabdomyosarcoma is one of the most common soft tissue sarcomas in adolescence and young adults. Histologically, rhabdomyosarcoma has many subgroups, including embryonal, alveolar, pleomorphic, and spindle cell/sclerosing rhabdomyosarcomas. More than 50% of embryonal rhabdomyosarcomas occur in the head and neck region. The retroperitoneum and pelvis are less common sites of involvement. Primary pulmonary embryonal rhabdomyosarcoma is extremely rare. A 3-year-old girl presented with symptoms of cough and shortness of breath. A mass lesion with regular contours, approximately 3x3 cm in size, containing millimetric air densities within, and having soft tissue density was detected in the upper lobe of the right lung. According to the results of bronchoscopy and biopsy, a right thoracotomy and right upper lobectomy were performed with the diagnosis of embryonal rhabdomyosarcoma. We present a case whose pathology confirmed the diagnosis of embryonal rhabdomyosarcoma.


1. Dasgupta R, Fuchs J, Rodeberg D. Rhabdomyosarcoma. Semin Pediatr Surg. 2016;25(5):276-283
2. Hafiz B, Bamefleh H. Primary pulmonary alveolar rhabdomyosarcoma in a pediatric patient: a case report with literature review. Cureus. 2022;14(1): e21270.
3. Taseer R, Ahmed TT. Embryonal rhabdomyosarcoma presenting as lung metastasis in an adult: an uncommon presentation. Cureus. 2021;13(2): e13545.
4. Leiner J, Le Loarer F. The current landscape of rhabdomyosarcomas: an update. Virchows Archiv. 2020;476(1):97-108.
5. Skapek SX, Ferrari A, Gupta AA, et al. Rhabdomyosarcoma. Nat Rev Dis Primers. 2019;5(1):1-19.
6. Vanhoenacker FM, De Schepper AM, Parizel PM, Gielen JL. Imaging of soft tissue tumors. Springer Science & Business Media. 2006.
7. Beverly Raney R, Walterhouse DO, Meza JL, et al. Results of the Intergroup Rhabdomyosarcoma Study Group D9602 protocol, using vincristine and dactinomycin with or without cyclophosphamide and radiation therapy, for newly diagnosed patients with low-risk embryonal rhabdomyosarcoma: a report from the Soft Tissue Sarcoma Committee of the Children’s Oncology Group. J Clin Oncol. 2011;29(10):1312-1318.
8. Iqbal Y, Abdullah MF, Al-Jadaan S, Trabichi H, Al Omari A, Al-Sudairy R. Embryonal rhabdomyosarcoma of the lung in a child: case report and literature review. Ann Saudi Med. 2002;22(1-2):91-93.
9. Chang HL, Rosenberg AE, Friedmann AM, Ryan DP, Masiakos PT. Primary pulmonary rhabdomyosarcoma in a 5-month-old boy: a case report. J Pediatr Hematol Oncol. 2008;30(6):461-463.
10. Özcan C, Çelik A, Ural Z, Veral A, Kandiloğlu G, Balik E. Primary pulmonary rhabdomyosarcoma arising within cystic adenomatoid malformation: a case report and review of the literature. J Pediatr Surg. 2001;36(7):1062-1065.
Volume 2, Issue 1, 2025
Page : 33-35
_Footer